Retroperitoneal Malignant Peripheral Nerve Sheath Tumour: A Rare Case Report


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DEĞER A. N. , BAYAR M. A. , ÇAYDERE M., Deger H., TAYFUR M.

JOURNAL OF CLINICAL AND DIAGNOSTIC RESEARCH, vol.9, no.9, 2015 (Journal Indexed in ESCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 9 Issue: 9
  • Publication Date: 2015
  • Doi Number: 10.7860/jcdr/2015/14169.6481
  • Title of Journal : JOURNAL OF CLINICAL AND DIAGNOSTIC RESEARCH

Abstract

Malignant nerve sheath tumours (MPNST) are rare neoplasias and retroperitoneal cases are fairly rare and clinically difficult to be detected, but they are very agressive neoplasias. MPNST are frequently seen in head, neck and upper extremities. In patients with NF1; MPNST, a poor-prognostic lesion, may result from a malignant degeneration of a former plexiform neurofibroma. It is necessary to be aware of a potential malignancy in patients diagnosed with plexiform neurofibroma.