A Case of Double-Inlet Left Ventricle Reaching Adulthood Without Surgery Opere Edilmeden Erişkinliğe Ulaşmış Çift Girişli Sol Ventrikül Olgusu
Turk Kardiyoloji Dernegi Arsivi, vol.54, no.4, pp.347-351, 2026 (ESCI, Scopus, TRDizin)
- Publication Type: Article / Article
- Volume: 54 Issue: 4
- Publication Date: 2026
- Doi Number: 10.5543/tkda.2025.67916
- Journal Name: Turk Kardiyoloji Dernegi Arsivi
- Journal Indexes: Emerging Sources Citation Index (ESCI), Scopus, Central & Eastern European Academic Source (CEEAS), EMBASE, Directory of Open Access Journals, TR DİZİN (ULAKBİM), Biomedical Reference Collection: Corporate Edition (EBSCO), Health Research Premium Collection (ProQuest)
- Page Numbers: pp.347-351
- Keywords: Congenital heart diseases, double-inlet left ventricle, pulmonary stenosis, single ventricle, ventricular septal defect
- Kütahya Health Sciences University Affiliated: Yes
Abstract
Double-inlet left ventricle (DILV) is a rare congenital heart defect, also referred to as a single-ventricle defect. It has a complex structure in which blood from both atria flows into a single ventricle, accounting for approximately 1.5% of all congenital heart diseases. A 37-year-old female patient with no prior history of cardiac disease visited our outpatient clinic for routine cardiological evaluation. Transthoracic echocardiography (TTE) was performed after a 3/6 pansystolic murmur was heard at the mesocardiac focus and a 3/6 systolic ejection murmur at the pulmonary focus on cardiac auscultation. The patient's TTE revealed that the atrioventricular valves opened into one ventricular chamber in four-chamber apical imaging. There was no noticeable interventricular septum, while a rudimentary right ventricle and a ventricular septal defect (VSD) were observed. A gradient of 38 mmHg was measured in the pulmonary valve, and mild-to-moderate pulmonary stenosis was present. In the transesophageal echocardiography (TEE), a rudimentary interventricular septum and right ventricle were observed. Because the patient did not have any symptoms or cyanosis, she was informed about the potential need for occasional infective endocarditis prophylaxis and phlebotomy, and close medical follow-up was planned. A double-inlet left ventricle is known as a severe congenital heart anomaly that is typically diagnosed symptomatically in childhood and requires surgical intervention. However, very rarely, asymptomatic cases without surgical intervention have been reported in the literature to reach adulthood.