Dental and anaesthesiological care of a patient with Rett syndrome congress

Vural,Vural Ç., Tütüncüler Sancak K., Hakiki H., Yurttutan M. E.

23rd International Conference on Oral and Maxillofacial Surgery, Kowloon, Hong Kong, 31 March - 03 April 2017, pp.375

  • Publication Type: Conference Paper / Summary Text
  • City: Kowloon
  • Country: Hong Kong
  • Page Numbers: pp.375
  • Kütahya Health Sciences University Affiliated: No


Rett syndrome (RS) is a neurological disease that occurs only in females and it manifests with mental retardation, seizures, movement disorders, autistic behaviour and abnormal breathing. Airway control is difficult due to limited mouth opening. Bruxism, oculogyric crises, parkinsonism and dystonia are also common, while myoclonus and choreoathetosis are seen infrequently. Respiratory and cardiac diseases, prolonged QT syndrome, diabetes mellitus and anaesthetic agent sensitivity are significant considerations for anaesthesiologist. These features lead to the need for special care. These children require a coordinated multi-specialist oriented health care. We present a 12-year-old female with Rett syndrome who required extraction of impact right canine teeth. Teeth grinding – bruxism, difficulties in chewing and swallowing, poor oral cavity hygiene, oral inflammation with hypertrophic gingiva were observed in intraoral examination. She had loss of consciousness, movement disorders, mental retardation, screaming fits, irritation, anger, self-abusing behaviour and limited mouth opening. Therefore, sedation anaesthesia was planned for surgical procedures. After standard monitorisation, patient sedated only with propofol due to more sensitive to anaesthetics. There was no complication during sedation. After surgery, patient was awakened after applying analgesic and transferred to recovery room.